Carnitine Deficiency MD Searchlight Role of L carnitine in the transport of long chain fatty acids through Download Scientific Diagram Carnitine is an essential cofactor for transport of long chain fatty acids into mitochondria, where oxidation takes place. Carnitine deficiency leads to depressed mitochondrial oxidation of fatty acids, resulting in storage of fat Carnitines as Mitochondrial Modulators of Oocyte and Embryo Bioenergetics Metabolism: The carnitine shuttle and fatty acid metabolism (practice) Khan Academy